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Lymphangioleiomyomatosis and other cystic interstitial lung diseases
Published in Muhunthan Thillai, David R Moller, Keith C Meyer, Clinical Handbook of Interstitial Lung Disease, 2017
Amanda T Goodwin, William YC Chang
Lymphocytic interstitial pneumonia (LIP) is characterized by lymphocytic infiltration of the lung parenchyma and alveoli (35). Ischaemia secondary to vascular obstruction, post-obstructive bronchial ectasia and bronchiolar compression cause cyst formation (35,36).
Test Paper 5
Published in Teck Yew Chin, Susan Cheng Shelmerdine, Akash Ganguly, Chinedum Anosike, Get Through, 2017
Teck Yew Chin, Susan Cheng Shelmerdine, Akash Ganguly, Chinedum Anosike
A 67-year-old man with a progressive restrictive pattern of pulmonary function test and increasing chest tightness was sent for an HRCT for characterisation. HRCT showed nodular septal thickening with further bronchovascular nodules and thickening. Which one of the following disorders is most likely to be the cause? PneumoconiosisLymphangitisLymphocytic interstitial pneumoniaHypersensitivity pneumonitisChurg–Strauss syndrome
G2-lymphocyte chromosomal radiosensitivity in patients with LPS responsive beige-like anchor protein (LRBA) deficiency
Published in International Journal of Radiation Biology, 2019
Hossein Mozdarani, Fatemeh Kiaee, Saba Fekrvand, Gholamreza Azizi, Reza Yazdani, Majid Zaki-Dizaji, Sahar Mozdarani, Sohail Mozdarani, Hassan Nosrati, Hassan Abolhassani, Asghar Aghamohammadi
According to previous studies, various pulmonary complications are reported as clinical manifestations presented among LRBA-deficient patients. These complications include: upper and lower respiratory tract infections, parenchymal lung abnormalities, persisting lymphocytic infiltrates, bronchiectasis, bronchiolitis obliterans organizing pneumonia (BOOP) and lymphocytic interstitial pneumonia (Shokri et al. 2016; Kostel Bal et al. 2017; Al Sukaiti et al. 2017). Similar to these findings, we observed pneumonia, bronchiectasis, sinusitis and otitis media among our studied patients. These complications increase the need for diagnostic computed tomography scan (CT scan), therefore exposing the patients to high doses of radiation. Serra et al. (Serra et al. 2011), claim that using radiation-free MRI technique as an alternative to CT scan in the evaluation of lung abnormalities among the radiosensitive primary immunodeficiency disorders is a possible solution for protecting the radiosensitive patients from unnecessary radiation.
Mucosa-associated lymphoid tissue lymphoma of parotid gland with involvement of subglottis and trachea
Published in Acta Oto-Laryngologica Case Reports, 2018
Natsumi Uehara, Naoki Otsuki, Hirotaka Shinomiya, Keiichiro Uehara, Ken-ichi Nibu
The close relationship between SS and malignant lymphomas has been known since 1963. SS has the strongest link with non-Hodgkin’s lymphoma (NHL) compared with other autoimmune diseases, such as systemic lupus erythematosus (SLE) and rheumatoid arthritis [5,13]. Voulgarelis et al. reported that NHL had 4.3% prevalence in patients with SS, and salivary glands were the most commonly affected site [14]. Twenty percent of the patients with SS displayed involvement of more than one extranodal site at first diagnosis, indicating that these lymphomas preferentially migrate to other mucosal sites. Thereby complete staging procedures are recommended in patients who have MALT lymphoma with SS. Moreover, it is well recognized that lymphoproliferative disorders in lungs, such as lymphocytic interstitial pneumonia, pseudolymphoma often observed in patients with SS [15]. Recently, almost these diseases are thought to be corresponded to MALT lymphoma and have known as bronchial-associated lymphoid tissue (BALT) lymphoma [16,17]. In this case, the parotid MALT lymphoma was not localized and involved larynx and trachea 7 months after the first noted SS.
Pulmonary involvement in primary Sjögren’s syndrome, as measured by the ESSDAI
Published in Scandinavian Journal of Rheumatology, 2020
A Heus, S Arends, JF Van Nimwegen, AJ Stel, GD Nossent, H Bootsma
In this large cross-sectional study, pulmonary involvement was found in 10–15% of the patients, comprising 10% assumed to be related to pSS and 5% possibly related to pSS. Most common was ILD, especially NSIP, followed by lymphocytic interstitial pneumonia and organizing pneumonia. UIP was not seen in any of the patients. Of all pSS patients, 6% were scored as active on the pulmonary domain of the ESSDAI, most with moderate activity. These findings underline the need for awareness of pulmonary involvement in patients with pSS in daily clinical practice.