Lipofibromatosis

Lipofibromatosis

Congenital Hand

Published in J. Terrence Jose Jerome, Clinical Examination of the Hand, 2022

Macrodactyly consists of a significant increase in the length and girth of most or all digits. Both the soft tissue and skeletal elements are diffusely enlarged in the affected digits. It is often associated with lipofibromatosis. The growth of the enlarged digit may be disproportionate (progressive type), or the digits may maintain a consistent proportion to the remainder of the hand (static type) [31].

Lipofibromatosis: Central Nervous System Involvement by a Benign Neoplasm

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Journal Information

Published in Fetal and Pediatric Pathology, 2023

Alejandra Rebolledo, Laura J. Guerra, Ander EO. Dubón, Mauricio Brindis

In conclusion, lipofibromatosis is a relatively new entity, considered in the differential diagnosis of soft tissue tumors in children, is typically a painless, slowly growing mass involving the extremities, cured with complete resection but tends to recur if removal is incomplete. Atypical forms have been described and their highly infiltrative capability can lead to the involvement of critical structures of the central nervous system.

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Journal Information

Published in Fetal and Pediatric Pathology, 2019

Kanika Rastogi, Lavleen Singh

Lipofibromatosis is a benign pediatric soft tissue tumor which should be considered in the differential diagnosis of a fibrofatty tumor in children, particularly when arising in the distal extremities. Complete surgical excision is the treatment of choice and incomplete removal may result in recurrence.

Lipofibromatosis

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Congenital Hand

Lipofibromatosis: Central Nervous System Involvement by a Benign Neoplasm

Lipofibromatosis