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Cardiovascular system
Published in Jagdish M. Gupta, John Beveridge, MCQs in Paediatrics, 2020
Jagdish M. Gupta, John Beveridge
8.10. Which of the following statements is/are correct?Tricuspid atresia is the most common type of cyanotic congenital heart disease.In tetralogy of Fallot the child typically adopts a squatting position after exertion.Notching of the ribs will not be seen in a 6-month-old infant with coarctation of the aorta.The murmur of atrial septal defect is due to flow across the defect.Stridor will resolve in more than 80% of cases by 3 months after surgical correction of vascular ring.
Heart disease
Published in Catherine Nelson-Piercy, Handbook of Obstetric Medicine, 2020
This results after surgery for tricuspid atresia or transposition with pulmonary stenosis. The right ventricle is bypassed and the left ventricle provides the pump for both the systemic and pulmonary circulations.Increases in venous pressure may cause hepatic congestion and oedema, but sufficient volume loading is required to ensure adequate perfusion of the pulmonary circulation.Assessment of liver disease/fibrosis is required before pregnancy.Women are often anticoagulated outside pregnancy and treatment or high prophylactic doses of LMWH are recommended during pregnancy.
The Child With Suspected Congenital Heart Disease
Published in Michael B O’Neill, Michelle Mary Mcevoy, Alf J Nicholson, Terence Stephenson, Stephanie Ryan, Diagnosing and Treating Common Problems in Paediatrics, 2017
Michael B O’Neill, Michelle Mary Mcevoy, Alf J Nicholson, Terence Stephenson, Stephanie Ryan
Tricuspid atresia results from abnormal formation of the tricuspid valve during foetal cardiac development. This usually presents with severe cyanosis and tachypnoea from birth. Examination reveals cyanosis, a systolic murmur at the lower left sternal border and a single second heart sound.
Monochorionic Twin Discordance for Horseshoe Lung and Tricuspid Atresia
Published in Fetal and Pediatric Pathology, 2022
Marina Sousa Gomes, José Monterroso, Otília Brandão, Carla Ramalho
Another important aspect to consider in this case is the association between horseshoe lung and tricuspid atresia. In general, the prognosis of horseshoe lung depends on the degree of pulmonary hypoplasia and the severity of associated cardiovascular malformations. Associations between atrioventricular septal defects, tetralogy of Fallot, coarctation of the aorta, patent ductus arteriosus, double inlet left ventricle, persistent left superior cava, and horseshoe lung have been described [3, 4]. In our fetus, the pulmonary horseshoe malformation coexisted with tricuspid atresia, an association not previously described. Tricuspid atresia has no right atrioventricular connection. The prognisis depends on the degree of right ventricle hypoplasia. In this case, there was no ventricular septal defect and the inlet portion of the right ventricle was absent. Consequently, there was a functionally univentricular heart.
Pulmonary artery banding in patients with functional single ventricle associated with pulmonary hypertension
Published in Clinical and Experimental Hypertension, 2021
Gang Li, Han Zhang, Xiangming Fan, Junwu Su
During the study, 97 patients with functional single ventricle anomalies and pulmonary hypertension undergoing PAB. There were 63 males, the median age at operation was 12(range 2 to 168) months and the mean weight was (11.7 ± 7.9) kg. 33 patients were diagnosed with single ventricle, 20 patients had tricuspid atresia, 17 patients had double-outlet right ventricle, 16 patients had transposition of the great arteries, and 8 patients had unbalanced atrioventricular septal defect. The specific morphology included right ventricular hypoplasia (n = 3), total anomalous pulmonary venous connection(n = 4). PAB was an isolated procedure in 86 patients, the remaining 11 patients received concomitant procedures, including PDA ligation (n = 6), atrioventricular valve repair(n = 5). Due to the limitation of previous working conditions and the economic hardship, only 30 patients received cardiac catheterization before PAB. We analysis the patients’ pulmonary artery pressure that who received cardiac catheterization, showed that echocardiography vs cardiac catheterization vs measured intraoperatively(64.28 ± 13.65; 59.57 ± 9.86; 59.53 ± 12.26 mmHg;p > .05), there were no significant statistical difference. The patients’ characteristics are summarized in Table 1.
Uni-ventricular pregnancy: a case report in a low resource country
Published in Journal of Obstetrics and Gynaecology, 2020
Bharat Bassaw, Dinesh Singh, Javed Chinnia, Abhinav Karan, Jonathan Ramsarran
Uni-ventricular cardiac disease accounts for 3.2% of congenital cardiac abnormalities (Theodoridis et al. 2005). The Fontan Procedure was initially performed for tricuspid atresia (Fontan and Baudet 1971) but, its indication has extended to include uni-ventricular disease. Successful pregnancy associated with this condition is rare, and a recognised cause of significant maternal mortality (de Swiet 2002). Given the deficiency of similar cases, optimal management of these patients remains contentious (Siu and Colman 2001).