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Tumors of the Nervous System
Published in Philip B. Gorelick, Fernando D. Testai, Graeme J. Hankey, Joanna M. Wardlaw, Hankey's Clinical Neurology, 2020
Other tumors/masses of the cerebellopontine angle: Meningioma.Trigeminal schwannoma.Cholesteatoma.Epidermoid cyst.Glomus tumor.Chordoma.Choroid plexus papilloma.
Anatomical and Biological Imaging of Pediatric Brain Tumor
Published in David A. Walker, Giorgio Perilongo, Roger E. Taylor, Ian F. Pollack, Brain and Spinal Tumors of Childhood, 2020
Rob A. Dineen, Shivaram Avula, Andrew C. Peet, Giovanni Morana, Monika Warmuth-Metz
Atypical choroid plexus papilloma was introduced into the WHO tumor classification in 2007 as a grade II tumor following recognition of an intermediate tumor entity falling between choroid plexus papillomas and carcinomas. In a large series of choroid plexus tumors, atypical choroid plexus papilloma was found to occur most frequently in the first year of life.164 These tumors are typically intraventricular but origin in the cerebellopontine angle is described. On MRI the tumor appears as a rounded or multilobulated mass with heterogeneous signal on T1- and T2-weighted images and strong or heterogeneous enhancement following administration of GBCA.165 Tumor margins may be blurred and there may be mild to moderate surrounding edema. Metastases are relatively common at presentation, being present in one series in 17%.164
Viral neuro-oncogenesis: Polyomaviruses and brain tumors
Published in Avindra Nath, Joseph R. Berger, Clinical Neurovirology, 2020
Martyn K. White, Sidney E. Croul, Kamel Khalili
Choroid plexus papilloma and carcinoma are rare CNS lesions that arise from the normal choroid plexus in the lateral, third, and fourth ventricles as circumscribed, cauliflower like masses. Not only do they obstruct ventricular outflow, they also oversecrete cerebrospinal fluid, and by both mechanisms they result in hydrocephalus.
Norrie disease with a spontaneously shrinking choroid plexus abnormality: a case report
Published in Ophthalmic Genetics, 2021
Subhi Talal Younes, James Mason Shiflett, Kristin Weaver, Andrew Smith, Betty Herrington, Charlotte Taylor, Kartik Reddy
As a whole, choroid plexus masses are rare in children, accounting for 1% or less of intracranial tumors in children. The most common choroid plexus lesions in children include choroid plexus cysts, choroid plexus papilloma, or choroid plexus carcinoma. Choroid plexus cysts are believed to arise from fluid trapping within the developing neuroepithelium (12). Estimated to be present in one to 2% of the population, such cysts require no intervention. Choroid plexus papilloma and carcinoma are neoplasms; as such, they require treatment. The former can be cured with surgery alone (13). The latter is typically a manifestation of an underlying cancer predisposition syndrome, most commonly, Li Fraumeni (14). These aggressive tumors require resection and adjuvant therapy, usually craniospinal irradiation or intensive chemotherapy regimens (15,16). Unfortunately, survival for choroid plexus carcinoma remains poor. For reasons explained above, none of these entities appeared to be the diagnosis in this patient.