Cardiovascular system
Jagdish M. Gupta, John Beveridge in MCQs in Paediatrics, 2020
8.23. Which of the following are associated with finger clubbing?Aortic coarctation.Tricuspid atresia.Tetralogy of Fallot.Asthma.Partial atrioventricular septal defect.
Cardiology
Rachel U Sidwell, Mike A Thomson in Concise Paediatrics, 2020
Atrioventricular septal defect (also known as A-V canal defect or endocardial cushion defect) is a severe form of CHD where there is a contiguous atrial and ventricular septal defect and defects of the mitral and tricuspid valves. (There are variable degrees of severity of AVSD.)
Prenatally diagnosed infracardiac total anomalous pulmonary venous connection: from the two sides of the spectrum
Published in Journal of Obstetrics and Gynaecology, 2018
Sezen Atik-Ugan, İrfan Levent Saltik
The foetus had been diagnosed as right atrial isomerism and complete atrioventricular septal defect at another centre on a routine obstetric scan. A 32-year-old healthy mother was referred to our clinic for a second opinion. On foetal echocardiography, which was performed in 21 weeks of gestation, the diagnosis of right atrial isomerism, complete atrioventricular septal defect and double outlet right ventricle were confirmed. In sagittal and transverse views at diaphragm level, an abnormal and additional vascular structure was identified. Detailed examination revealed that pulmonary veins did not open into the left atrium and formed a common vertical descending vein (Figure 1(F)). This vertical vein showed an infra diaphragmatic course and the foetus diagnosed as infracardiac TAPVC. The delivery took place in another hospital and diagnosis confirmed by postnatal echocardiographic examination. The baby died while waiting for surgery.
Characteristics of prenatally detected right aortic arch cases in a single institution
Published in Journal of Obstetrics and Gynaecology, 2018
Melih Velipasaoglu, Metin Sentürk, Reyhan Ayaz, Barbaros Atesli, H. Mete Tanir
The total number of patients who were scanned during the study period (18 months) was 6632. A total of 228 foetuses with major anomalies were diagnosed in this low-risk group of patients with an incidence of 3.4%. Of these foetuses, 75 had major cardiac anomalies (32.8%). There were 12 cases of RAA detected prenatally. All cases were in singleton pregnancies. The prevalence in the study population was 1.8 in 1000 and constituted 16% of all major cardiac anomalies within the study cohort. Patient characteristics are presented in Table 1. The mean age of the patients was 30.4 (±3.9) years. The mean gestational age at diagnosis was 20.9 (±1.9) weeks. The only associated cardiac anomaly was atrioventricular septal defect (AVSD) in one foetus (8.3%). The only associated major extra-cardiac anomaly was oesophageal atresia in the same foetus with AVSD (8.3%).
Preventing disease progression in Eisenmenger syndrome
Published in Expert Review of Cardiovascular Therapy, 2021
Ana Barradas-Pires, Andrew Constantine, Konstantinos Dimopoulos
The ECG is fundamental to the assessment and follow-up of ES patients. Indeed, ventricular or atrial arrhythmias can lead to rapid clinical decompensation, and are a predictor of outcome in PAH-CHD [24]. Common features include signs of right ventricular hypertrophy (dominant R wave in lead V1 and right QRS axis deviation) and right atrial enlargement (so-called ‘P pulmonale’; Figure 1). The typical feature observed in patients with ES associated with an atrioventricular septal defect is a left axis deviation (or an extreme right superior axis deviation), caused by displacement of the conduction system.
Related Knowledge Centers
- Atrioventricular Septum
- Interatrial Septum
- Interventricular Septum
- Shortness of Breath
- Atrial Septal Defect
- Ischemia
- Cyanosis
- Heart
- Endocardial Cushions
- Ventricular Septal Defect
- Shortness of Breath